Story: Hemophilia appeared in the British royal family in the19th century, and it spread to all the royal families in Europe. Victoria Victoria as the grandmother of Europe, is one of the most famous hemophiliacs in history. She has nine children: 1.3.5.6.9 is a daughter and 2.4.7.8 is a son. Among the daughters, (3) Helena Alice, (9) Beatrice is a hemophiliac; The eighth son, Leopold Leopold, is a hemophiliac. Leopoldt Leopold is in Ireland, and one of his grandchildren is a hemophiliac. Helena Alice married a grandson of Louis II, Duke of Hesse in the German Empire, and brought hemophilia to the Hesse family. Her daughter Irene also became a hemophilia gene carrier. Irene's husband is the eldest daughter of Victoria (1) and the son of the German emperor. Although the prince himself is normal, he brought the hemophilia gene to the Prussian family because of his marriage with Irene. Helena Alice)3 also has a daughter Alix at the age of 3 and is also a carrier. She married Russian Tsar Nicholas II, which caused the Tsar's son to suffer from hemophilia. Beatrice (9 years old) married another grandson of Louis II, the grand duke of Hesse, and brought the hemophilia gene to another branch of the Hesse family. Her daughter Victoria is also a carrier. She married King Alfonso XIII of Spain, thus bringing the hemophilia gene into the Spanish royal family.
Now Queen Elizabeth II is a descendant of Edward VII, the son of Victoria. Edward VII did not have hemophilia, so his descendants will not have hemophilia. Elizabeth II's husband Philip is a descendant of Alice's eldest daughter. Fortunately, the eldest daughter is not a carrier, so the British royal family should not suffer from hemophilia again.
In fact, this genetic nature of hemophilia has long been known. Since ancient times, it has been explained in the Jewish legal work Talmud, which has always been regarded as the sacred norm of Judaism; Hemophilia is passed on from mother to some of her children. The law even stipulates that mothers who have lost two baby boys to excessive blood loss are not allowed to participate in the "circumcision" ceremony. 1820, the German doctor Nasser observed hemophilia and established the so-called "Nasser's Law": hemophilia only appears in men, but is inherited by women. Dr Otto also pointed out that hemophilia is a familial disease. Men are the main body of this disease, while women are not, but it will be passed on to their children through women. ...
Of course, the doctors of emperors in past dynasties will not be ignorant of this understanding or conclusion about hemophilia. The royal family obviously ignored all this for political needs.
According to the above story, hemophilia is a group of hereditary hemorrhagic diseases. But according to the lack of coagulation factors, it is divided into:
Hemophilia A (A): lack of coagulation factor VIII. Hemophilia B (B): lack of coagulation factor IX.
Hemophilia c: lack of the eleventh coagulation factor.
There is one hemophilia patient per 10,000 people in the total population, of which type A accounts for about 80%~85%, and type B accounts for about 15% ~ 20%. Among them, 1/3 cases are caused by gene mutation, and there are also acquired hemophilia patients. Hemophilia C is rare, with mild symptoms, which belongs to individual recessive inheritance, and both men and women will have symptoms. Hemophilia patients often have spontaneous or periodic bleeding all their lives; There may be no reason, but the general clinical manifestations are:
Bleeding is the main manifestation of this disease. Bleeding site: Generally, it is gum, tongue, mouth and nose. Bleeding of knee, ankle and elbow joint is its characteristic and the most common. For several months or years, joint stiffness, deformity and muscle atrophy will occur, resulting in loss of function. In severe cases, visceral bleeding sometimes occurs, such as gastrointestinal bleeding and urinary tract bleeding. Intracranial bleeding caused by head trauma is often the main cause of death.
Hemophilia is a life-long hemorrhagic disease. Prenatal examination should be carried out for carriers, and the fertility of children and carriers should be controlled, so as to reduce the morbidity of the population and achieve eugenics.
There is no cure for hemophilia at present. Therefore, we should pay attention to "comprehensive treatment". In addition to the corresponding infusion of various coagulation factor products during bleeding, traditional Chinese medicine plays an active role in the rehabilitation after bleeding and the treatment and prevention of hemophilic arthritis.
● Drug introduction:
Internal medicine:
Sanguis Draxonis Liu Ling Powder is a pure Chinese medicine preparation, which is specially developed for hemophilia and hemorrhagic diseases. It can improve coagulation quality and enhance hematopoietic activity. Suitable for gastrointestinal bleeding, joint bleeding, mucosal and skin bleeding, thrombocytopenic purpura and other bleeding.
Youtai capsule is a pure Chinese medicine preparation: specially developed for hemorrhagic diseases. Regulating qi and blood, stopping bleeding, dredging menstruation, removing blood stasis and freckle, and enhancing immune function. Suitable for hemophilia and various hemorrhagic diseases. External use:
Guanjieling is a pure Chinese medicine preparation: it is used to treat hemophilia, joint bleeding, pain and dyskinesia. Also has good curative effect on treating various arthritis.
If you or your relatives and friends are willing to receive treatment, please bring or send the patient's medical records, laboratory tests and other materials (copies are also acceptable) so as to understand the patient's detailed illness and related medical history, so that we can better treat you. There is a special person in charge of reception and mail order.
● Self-care:
Self-care of hemophiliacs is very important. After the bleeding stops, after a period of bed rest, you can do some slight self-care massage appropriately. This will be beneficial to the health of the disease and the recovery of the disabled limb function. Introduce the practical experience of some patients: (mainly knee, ankle and elbow)
Principle: A: Only after the bleeding stops. B: Don't push, rub, rub and hit. C: You can't stretch or bend hard. D: Be sure to do it often and for a long time.
Operation: touch, twist and flap evenly and gently.
Knee joint: Sit on the bed, protect the knee joint with both hands, and gently knead with both hands except thumb and fingers. Consciously do stretching and bending exercises. Touch thighs, joints, calves and toes. Gently pat the calf muscles. Hand elbow joint: Gently touch the arm from top to bottom with a bloodless hand, and gently twist the upper arm and forearm to the wrist. (It is best to massage your back a little)
Ankle: Gently touch, rub and move the ankle.
The above skills can only be done step by step, starting with low intensity, short duration and low amount of exercise. With the improvement of the disease, physical strength increases, and the sports indicators gradually improve after skillful movements.
These are all ways to take care of yourself, and it will be more pleasant if someone can help.
● Psychology and emotion
The psychological and emotional qualities of hemophilia patients can also directly affect the occurrence of the disease. Hemophilia patients bear different psychological activities from ordinary patients, and because of the particularity of the disease, they have caused heavy psychological and spiritual burdens to themselves and their relatives. Therefore, patients must cultivate their own good psychological coping mechanism and control their emotions. Now I will briefly summarize the experiences of some patients:
A: Don't be lazy on the grounds of illness.
B: Accept yourself happily, eliminate inferiority, and live in harmony with the surroundings.
C: Enhance self-confidence and believe that you have the ability to get rid of or alleviate the pain of illness.
D: Do what you can, and don't force the impossible.
E: Have more hobbies and cultivate your good taste.
F: Follow your heart.
G: Don't shut yourself off and lead a reckless life, but don't indulge.
H: Think calmly and don't be impatient.
● Beverage and food:
"Illness from the mouth" pays attention to the rational distribution of meals, grasps the nutritional characteristics of various foods, and adjusts their position and proportion in the diet, which has a positive effect on the health of hemophiliacs.
Principle:
A: Try to avoid or eat less food that is harmful to the coagulation mechanism and irritating food.
B: Eat more foods that are good for spleen, liver, kidney and blood.
Generally beneficial foods are peanuts, red dates, fresh lotus root, day lily, eggplant, bitter gourd, kumquat, tomato, black sesame, chicken, duck, pig, sheep, cattle, turtle, turtle, eel and so on.
Foods that are useless or less eaten are: all kinds of raw seafood, freshwater fish and all kinds of fried foods. Tobacco, wine, tea, betel nut.
Avoid drinking chicken soup and fresh meat soup when bleeding from digestive tract. It is best to refuse the entrance of acidic food.
Traditional Chinese medicine believes that this disease belongs to blood heat, and you can eat more cold food in your diet. )
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